Double outlet right ventricle with spontaneously developing pulmonary outflow obstruction.

Double outlet right ventricle with pulmonary stenosis.

Although transposition of the great vessels is a well-known clinical and pathological entity, the partial transposition complex, resulting in the origin of both the aorta and the pulmonary trunk from the right ventricle, is rare. The association of this malformation with pulmonary stenosis has been described previously (Braun et al., 1952; Witham, 1957; Neufeld, DuShane, and Edwards, 1961; Morg...

Double outlet right ventricle.

double-outlet right ventricle

In a previous study the possibility that tetralogy of Fallot and transposition of the great arteries may arise as a result of embryonic arrests in the normal rotation of the junction of the outflow tract and the great arteries was investigated. The results suggested that the development of other transposition complexes such as double-outlet right ventricle might also be related to arrests in th...

Surgical Management of Left Ventricular Outflow Tract Obstruction after Biventricular Repair of Double Outlet Right Ventricle

Regardless of the preoperative morphology and the type of operation, left ventricular outflow tract obstruction (LVOTO) after biventricular repair of double outlet right ventricle (DORV) may develop. This report presents our 10-yr experience with surgical management of LVOTO after biventricular repair of DORV. Between 1996 and 2006, 15 patients underwent reoperation for subaortic stenosis after...

Right ventricular outflow tract stenting in double outlet right ventricle with critical pulmonary stenosis and hypoplastic pulmonary arteries

Double outlet right ventricle (DORV) is a congenital heart disease in which the great arteries (aorta and main pulmonary artery) arise from the right ventricle (RV), with concomitant ventricular septal defect (VSD), usually non-restrictive. Double outlet right ventricle can be accompanied by other cardiovascular anomalies, such as ventricular hypoplasia, restrictive septal defects and various p...